Sjogren syndrome is a chronic disorder affecting the exocrine glands of the body, mostly lacrimal and salivary glands, resulting in sicca symptoms. Diagnosis is aided by the presence of anti-Ro and anti-La antibodies and gland biopsy showing lymphocytic infiltration. Bilateral loss of facial sensation in Sjogren syndrome (SS) has not been reported before, although unilateral trigeminal palsy as a presentation of SS has been reported in literature. A 25-year-old lady presented in the neurology clinic with complete facial numbness and vision loss for 1 month. The vision worsened, leading to complete blindness. She had dry mouth and dry eyes for the past 3 months. She was diagnosed with SS using American–European consensus Sjogren criteria. Electrophysiological blink reflex testing confirmed complete trigeminal nerve palsy. SS was treated with prednisolone, 1 mg/kg/day, with a poor response. Symptomatic treatment was given for sicca symptoms, which improved significantly. Corneal transplantation was done for visual loss, but limited improvement was seen.
Ilyas, A., Malik, W. T., Abrar, A., & Zafar, F. (2017). A rare case of bilateral trigeminal palsy presenting as a complication of Sjogren syndrome. Kasr Al Ainy Medical Journal, 23(1), -. doi: 10.4103/kamj.kamj_57_16
MLA
Ali Ilyas; Wasim T. Malik; Anam Abrar; Faleha Zafar. "A rare case of bilateral trigeminal palsy presenting as a complication of Sjogren syndrome", Kasr Al Ainy Medical Journal, 23, 1, 2017, -. doi: 10.4103/kamj.kamj_57_16
HARVARD
Ilyas, A., Malik, W. T., Abrar, A., Zafar, F. (2017). 'A rare case of bilateral trigeminal palsy presenting as a complication of Sjogren syndrome', Kasr Al Ainy Medical Journal, 23(1), pp. -. doi: 10.4103/kamj.kamj_57_16
VANCOUVER
Ilyas, A., Malik, W. T., Abrar, A., Zafar, F. A rare case of bilateral trigeminal palsy presenting as a complication of Sjogren syndrome. Kasr Al Ainy Medical Journal, 2017; 23(1): -. doi: 10.4103/kamj.kamj_57_16
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